| Early pulmonary inflammation in infants with cystic fibrosis. TZ Khan, JS Wagener, T Bost, J Martinez, FJ Accurso, DW Riches American journal of respiratory and critical care medicine 151 (4), 1075-1082, 1995 | 1629 | 1995 |
| Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report PM Farrell, BJ Rosenstein, TB White, FJ Accurso, C Castellani, ... The Journal of pediatrics 153 (2), S4-S14, 2008 | 1288 | 2008 |
| Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial L Saiman, BC Marshall, N Mayer-Hamblett, JL Burns, AL Quittner, ... Jama 290 (13), 1749-1756, 2003 | 1211 | 2003 |
| Diagnosis of cystic fibrosis: consensus guidelines from the cystic fibrosis foundation PM Farrell, TB White, CL Ren, SE Hempstead, F Accurso, N Derichs, ... The Journal of pediatrics 181, S4-S15. e1, 2017 | 938 | 2017 |
| Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation FJ Accurso, SM Rowe, JP Clancy, MP Boyle, JM Dunitz, PR Durie, ... New England Journal of Medicine 363 (21), 1991-2003, 2010 | 915 | 2010 |
| Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation JP Clancy, SM Rowe, FJ Accurso, ML Aitken, RS Amin, MA Ashlock, ... Thorax 67 (1), 12-18, 2012 | 651 | 2012 |
| Elastase-mediated phosphatidylserine receptor cleavage impairs apoptotic cell clearance in cystic fibrosis and bronchiectasis RW Vandivier, VA Fadok, PR Hoffmann, DL Bratton, C Penvari, KK Brown, ... The Journal of clinical investigation 109 (5), 661-670, 2002 | 553 | 2002 |
| Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis D Borowitz, KA Robinson, M Rosenfeld, SD Davis, KA Sabadosa, ... The Journal of pediatrics 155 (6), S73-S93, 2009 | 472 | 2009 |
| Molecular identification of bacteria in bronchoalveolar lavage fluid from children with cystic fibrosis JK Harris, MA De Groote, SD Sagel, ET Zemanick, R Kapsner, C Penvari, ... Proceedings of the National Academy of Sciences 104 (51), 20529-20533, 2007 | 426 | 2007 |
| Defective lipoxin-mediated anti-inflammatory activity in the cystic fibrosis airway CL Karp, LM Flick, KW Park, S Softic, TM Greer, R Keledjian, R Yang, ... Nature immunology 5 (4), 388-392, 2004 | 416 | 2004 |
| Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis M Rosenfeld, J Emerson, F Accurso, D Armstrong, R Castile, K Grimwood, ... Pediatric pulmonology 28 (5), 321-328, 1999 | 390 | 1999 |
| Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis RL Gibson, J Emerson, S McNamara, JL Burns, M Rosenfeld, A Yunker, ... American journal of respiratory and critical care medicine 167 (6), 841-849, 2003 | 386 | 2003 |
| Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial E Kerem, MW Konstan, K De Boeck, FJ Accurso, I Sermet-Gaudelus, ... The Lancet Respiratory Medicine 2 (7), 539-547, 2014 | 377 | 2014 |
| The metabolic and molecular basis of inherited disease MJ Welsh, BW Ramsey, F Accurso, GR Cutting, CR Scriver, AL Beaudet, ... | 333 | 2001 |
| Restoring cystic fibrosis transmembrane conductance regulator function reduces airway bacteria and inflammation in people with cystic fibrosis and chronic lung infections KB Hisert, SL Heltshe, C Pope, P Jorth, X Wu, RM Edwards, M Radey, ... American journal of respiratory and critical care medicine 195 (12), 1617-1628, 2017 | 325 | 2017 |
| Repeated aerosolized AAV-CFTR for treatment of cystic fibrosis: a randomized placebo-controlled phase 2B trial RB Moss, C Milla, J Colombo, F Accurso, PL Zeitlin, JP Clancy, ... Human gene therapy 18 (8), 726-732, 2007 | 325 | 2007 |
| Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis H Corvol, SM Blackman, PY Boëlle, PJ Gallins, RG Pace, JR Stonebraker, ... Nature communications 6 (1), 8382, 2015 | 295 | 2015 |
| Role of respiratory syncytial virus in early hospitalizations for respiratory distress of young infants with cystic fibrosis SH Abman, JW Ogle, N Butler-Simon, CM Rumack, FJ Accurso The Journal of pediatrics 113 (5), 826-830, 1988 | 286 | 1988 |
| Pulmonary vascular response to oxygen in infants with severe bronchopulmonary dysplasia SH Abman, RR Wolfe, FJ Accurso, BL Koops, CM Bowman, ... Pediatrics 75 (1), 80-84, 1985 | 275 | 1985 |
| Association between pulmonary function and sputum biomarkers in cystic fibrosis N Mayer-Hamblett, ML Aitken, FJ Accurso, RA Kronmal, MW Konstan, ... American journal of respiratory and critical care medicine 175 (8), 822-828, 2007 | 269 | 2007 |
